NettetLinear and whorled nevoid hypermelanosis is characterized by diffuse streaks and swirls rather than localized hyperpigmented lesions as in progressive cribriform and zosteriform hyperpigmentation. In addition, linear and whorled nevoid hypermelanosis has an early age of onset with gradual spread during the first 2 years of life with … Nettet4. jul. 2024 · 5. Zeng L, et al. Familial progressive hyperpigmentation and hypopigmentation without KITLG mutation. Clin Exp Dermatol 2016; 41: 927-9. 6. Sorlin A, et al. Mosaicism for a KITLG mutations in linear and whorled nevoid hypermelanosis. J Invest Dermatol 2024; 137: 1575-78. 7.
Congenital and inherited hyperpigmentation disorders - UpToDate
Nettet5. nov. 2024 · What’s your diagnosis? Answer: Linear and whorled nevoid hypermelanosis. Linear and whorled nevoid hypermelanosis is a rare sporadic disorder with no gender predominance [1].They are other synonyms in the literature: Linear nevoid hyperpigmentation, reticulate hyperpigmentation of Iijima, Naito, and Uyeno, and … NettetLinear and whorled nevoid hypermelanosis (LWNH) is a rare skin condition characterized by swirling streaks of hyperpigmented (darkened) skin. The pigmentation follows the lines of Blashko and is mainly located on the trunk and limbs. It is present at birth or appears in the first few weeks of life. It typically progresses for one to two years and then stabilizes. glittering points that downward thrust riddle
Linear and whorled nevoid hypermelanosis - Wikipedia
Nettet1. feb. 2009 · Linear and whorled nevoid hypermelanosis (LWNH) is a sporadic pigmentary disorder reported initially by Kalter et al1 in 1988. The syndrome is characterized by swirls and streaks of macular hyperpigmentation following the lines of Blaschko without any preceding inflammatory or palpable verruciform lesions. The … Nettet10. jan. 2024 · Aradhana Sood. Linear and whorled nevoid hypermelanosis (LWNH) is a rare disorder of pigmentation characterized by hyperpigmented macules in a linear or … Nettet3. okt. 2024 · Patterned pigmentation describes a phenotype in which the skin has lighter or darker shades in a particular pattern. The skin pigmentation can either be isolated or signal an underlying disorder … glittering prizes book